"Mystery brain disorder robs patients of their words"

AP: It's called primary progressive aphasia, and researchers said Sunday they're finding better ways to diagnose the little-known syndrome. That will help people whose thoughts are lucid but who are verbally locked in to get the right kind of care.

"I'm using a speech device to talk to you," Robert Voogt of Virginia Beach, Virginia, said by playing a recording from a phone-sized assistive device at a meeting of the American Association for the Advancement of Science. "I have trouble speaking, but I can understand you."

PPA wasn't identified as a separate disorder until the 1980s, and while specialists estimate thousands of Americans may have it, there's no good count. Families may not even seek care because they assume a loved one's increasingly garbled attempts to communicate are because of age-related dementia, said Dr. Argye Elizabeth Hillis of Johns Hopkins University. Often, it's when those people reach neurologists who realize they aren't repeating questions or forgetting instructions that the diagnosis emerges.

"Nobody's talking to them, nobody's involving them. It's very sad," said Dr. Margaret Rogers of the American Speech-Language-Hearing Association. Yet for many, "they can handle their own finances, they can drive, they can appreciate music. There's a lot that still works for them."

Speech and language are hugely complex. Just to speak requires activating 100 muscles between the lungs and lips to produce at least 14 distinct sounds per second, said Dr. Joseph Duffy of the Mayo Clinic. 

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